[MIM*133190] A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetric progressive erythrokeratodermia is inherited as an autosomal dominant disorder and does not involve the palms and soles. [erythro- + G. keras, horn, + derma, skin, + -ia, condition]