(ha´ welz´) an autosomal dominant syndrome of ectodermal dysplasia, cleft lip and palate, and ankyloblepharon filiforme adnatum; it is also characterized by hypodontia, palmar and plantar keratoderma, partial anhidrosis, sparse wiry hair, and sometimes otologic defects. Called also AEC syndrome and ankyloblepharon–ectodermal dysplasia–clefting syndrome.