This is a chronic, recurrent skin disease characterized by spontaneously regressing papules composed of an atypical CD30-positive T-cell population. The disease is defined as an atypical lymphoproliferative process and usually has a benign course. However, a minority of cases are clonal and can progress to frank lymphoma. Low dose methotrexate and psoralen/UVA (PUVA) are the best available therapies. (WHO, 2001) -- 2003
